Progressive symmetrical erythrokeratodermia - Case report*
نویسندگان
چکیده
Progressive symmetrical erythrokeratodermia is a rare autosomal dominant genodermatosis with variable penetrance described by Darier in 1911. It is characterized by erythematous and keratotic plaques, sharply defined and symmetrically distributed along the extremities, buttocks and, more rarely, on the face. We report a case of a 55-year-old patient with lesions on the dorsum of the hands, interphalangeal pads, wrists, groin and back feet. This case demonstrates a rare and late diagnosis, clinical profusion and presence of familiar involvement.
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1. Griffiths WA, Leigh IM, Marks R. Disorders of keratinization. In: Champion RH ,Burton JL, Ebling FJ, editors. Textbook of Dermatology. 5th ed. Oxford: Oxford Blackwell Scientific Publications; 1992. p. 1349-50. 2. Chu DH, Arroyo MP. Progressive and symmetric erythrokeratoderma. Dermatol Online J 2003;9:21. 3. Ghorpade A, Ramanan C. Progressive symmetric erythrokeratoderma. Ind J Dermatol Ven...
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